Volume 22, Issue 91 (8-2012)                   J Mazandaran Univ Med Sci 2012, 22(91): 111-114 | Back to browse issues page

XML Persian Abstract Print

Download citation:
BibTeX | RIS | EndNote | Medlars | ProCite | Reference Manager | RefWorks
Send citation to:

Nabati M, Ardavan K, Saliminia A, Babai A. Situs Ambigus, Right Isomerism (Asplenia syndrome). J Mazandaran Univ Med Sci. 2012; 22 (91) :111-114
URL: http://jmums.mazums.ac.ir/article-1-1302-en.html
Abstract:   (12931 Views)
When abdominal and thorasic organs are inversed it is called situs inversus and when most of the these organs are positioned abnormally and heterogenic It is called situs ambigus (Heterotoxy syndrome) which is a rare congenital defect (Incidence 1.44 in 100/000 live birth) In these, abnormal organs shift which could be to the Right side or left side (Right Isomerism, Left Isomerism). One of the Heterotoxy main subgroups is Right Isomerism, asplenia which is accompanied with centrally located liver, asplenia, two morphologic Right side lungs. Our case is 19 years old gril with central and peripheral cyanosis and clubbing from several years ago who had several recurrent pulmonary infection from childhood with history of PA banding surgery. She had dextrocardia, asplenia and cardiac abnormality were detected in CXR, echocardiography and sonography. Management of this abnormality include surgical correction and prevention of infection with vaccination and antibiotic prophylaxis due to asplenia.
Full-Text [PDF 345 kb]   (3455 Downloads)    
Type of Study: Research(Original) |

Add your comments about this article : Your username or Email:

© 2021 All Rights Reserved | Journal of Mazandaran University of Medical Sciences

Designed & Developed by : Yektaweb