The term amelogenesis imperfecta (AI) describes a diverse group of hereditary conditions primarily affecting the quality and/or quantity of dental enamel which are usually not associated with generalized findings. It affects all teeth in both the primary and permanent dentitions. The estimated frequency of AI is one in 14000. Disruptions occurring during histodifferentiation, apposition, and mineralization result in enamel hypoplasia or hypomineralization for AI. In this paper a 10-year-old male is presented who referred to a dental office in Sari with a chief complaint of generalized discolored teeth since childhood and sensitivity while having hot and cold foods. After clinical and radiographic examination the patient was diagnosed with AI (hypoplastic type). AI affects the psychology of patients negatively due to the aesthetic concerns, so, it should be identified promptly and involved patients must receive appropriate treatments.